Hereditary ectodermal dysplasia: a case report.
نویسنده
چکیده
Hereditary ectodermal dysplasia is an inherited disorder involving skin, hair, nails and teeth. Two main clinical forms have been described--hypohidrotic type and hidrotic type. A case of ectodermal dysplasia with absence of hypohidrosis and defective nails has been reported. The importance of early prosthetic management has been discussed.
منابع مشابه
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Ectodermal dysplasia is an extremely rare genetic disorder characterized by faulty development of ectodermal structures. The tissues in which the primary defects occur are the skin, hair, nails, exocrine glands, and teeth. It usually affects the males and females are the carriers. The clinical features include sparse hair, abnormal or missing teeth, and inability to sweat due to lack of sweat g...
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عنوان ژورنال:
- Journal of the Indian Society of Pedodontics and Preventive Dentistry
دوره 20 1 شماره
صفحات -
تاریخ انتشار 1987